Correlation Engine 2.0
Clear Search sequence regions

Longer survival after corrective surgery for congenital heart diseases has rendered late complications more important. One of these complications is aortic dilatation which may occur in patients with repaired or unrepaired disease and can progress to aneurysm, dissection, and rupture. This aortic dilatation in various congenital heart diseases does not simply mean anatomical dilatation of the aortic root, but it closely relates to the aortic pathophysiological abnormality, aortic regurgitation, and aortic and ventricular dysfunction; therefore, we can recognize this complex lesion as a new concept: "aortopathy". The pathophysiology of this disease is complex and only partially understood. In this review, we first discuss history, pathophysiology, and clinical features of aortic dilatation and aortopathy of congenital heart disease. Then we provide a review of the evaluation and management of this disease. Copyright © 2012 Japanese College of Cardiology. Published by Elsevier Ltd. All rights reserved.


Keyhan Sayadpour Zanjani, Koichiro Niwa. Aortic dilatation and aortopathy in congenital heart diseases. Journal of cardiology. 2013 Jan;61(1):16-21

Expand section icon Mesh Tags

Expand section icon Substances

PMID: 23177793

View Full Text