A Misdiagnosed Case of Double Outlet Right Atrium Associated With Hypoplastic Right Ventricle.

Double outlet right atrium (DORA) is a rare congenital heart disease in which the right atrium opens into both ventricles. The reduced leftward motion of the interventricular septum causes a malalignment between the atrial and the ventricular septum at the cardiac crux, which is the pathognomonic feature of this heart defect. We describe a case of significant exertional desaturation in an adult patient who was diagnosed with DORA, restrictive right ventricle, and anomalous tricuspid valve. Subsequently, the patient underwent one-and-a-half ventricular palliation.

Citation

Irene Raso, Andrea Quarti, Massimo Chessa, Domenica Paola Basile, Antonio Saracino, Angelo Fabio D'Aiello, Claudia Raineri, Mario Carminati, Alessandro Giamberti. A Misdiagnosed Case of Double Outlet Right Atrium Associated With Hypoplastic Right Ventricle. World journal for pediatric & congenital heart surgery. 2020 May;11(3):358-360

Mesh Tags

PMID: 32294022

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