Iliopsoas Hematomas in a Patient with Progressive Encephalomyelitis with Rigidity and Myoclonus.

Rui Shimazaki, Masako Mukai, Utako Nagaoka, Keizo Sugaya, Kazushi Takahashi

Internal medicine (Tokyo, Japan) 2021 Aug 01

filter terms:

Progressive encephalomyelitis with rigidity and myoclonus (PERM) is a rare and severe syndrome characterized by rigidity of the limb and truncal muscles, brainstem signs, myoclonus, and hyperekplexia. Iliopsoas hematoma is a serious complication of bleeding disorders that occurs most commonly in patients with hemophilia and also in association with anti-coagulant drug treatment. We herein present a case of PERM complicated with bilateral iliopsoas hematomas. His neurological symptoms improved after immunotherapy, and thereafter the iliopsoas hematomas disappeared. Neurologists should consider iliopsoas hematomas as a serious potential complication of PERM.

Citation

Rui Shimazaki, Masako Mukai, Utako Nagaoka, Keizo Sugaya, Kazushi Takahashi. Iliopsoas Hematomas in a Patient with Progressive Encephalomyelitis with Rigidity and Myoclonus. Internal medicine (Tokyo, Japan). 2021 Aug 01;60(15):2475-2477