Dermatofibrosarcoma Protuberans Of Trunk In A Male Patient.

Dermatofibrosarcoma protuberans is a rare cutaneous malignancy. Usual sites of origin are trunk and extremities. Aetiology of the condition is not well understood but a genetic basis is explained as a reciprocal translocation t (17l;22) (q22; q13). Distant metastasis is quite rare as it is mostly a locally advancing tumour. Histopathology is the most accurate investigation to make a diagnosis. Imaging is still required to rule out distant metastasis. Surgical excision is the treatment option for stage I tumours. Imatinib, a tyrosine kinase inhibitor, has shown promising results in management of locally advanced and metastatic disease.

Citation

Junaid Zia Hashmi, Ammarah Ghafoor, Masood Ur Rauf Khan Hiraj, Waseem Abbas Chaudhary. Dermatofibrosarcoma Protuberans Of Trunk In A Male Patient. Journal of Ayub Medical College, Abbottabad : JAMC. 2022 Apr-Jun;34(2):364-365

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PMID: 35576304

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