A girl in early adolescence with autism presented with 3 months of abdominal pain and 36 hours of anuria. She had recently received treatment for urinary tract infections, anxiety and menorrhagia (she had undergone menarche a few months earlier). Due to the pain, she had pulled out an incisor. Bladder scan showed 923 mL, creatinine was 829 mmol/L but urethral catheter insertion did not drain urine. An unenhanced CT scan revealed an absent left kidney, didelphys uterus and right-sided hydroureteronephrosis caused by haematocolpos in keeping with a diagnosis of OHVIRA syndrome and ureteric obstruction of a single kidney causing acute renal failure. She underwent vaginal septoplasty, drainage of the haematocolpos and right ureteric stent. © BMJ Publishing Group Limited 2024. No commercial re-use. See rights and permissions. Published by BMJ.
Joel Corkill, Simon Rupret, Emma Scrivens, Ayman Ali. A Novel cause of abdominal pain presenting with anuria and renal failure. BMJ case reports. 2024 Jan 29;17(1)
PMID: 38286586
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