Primary lung low-grade fibromyxoid sarcoma: A rare case with A diagnostic dilemma.

Low-grade fibromyxoid sarcoma (LGFMS) is a rare, low-grade malignant soft tissue tumor that is often mistaken for benign or more rarely malignant tumor types. Commonly, this tumor affects young adults and typically arises in the deep proximal extremities or trunk with frequent recurrences and can metastasize to the lungs many years late. Visceral LGFMS is extremely rare. Only a few cases of primary LGFMS of the lung have been reported. Here, we present the clinical, gross, microscopic, and immunohistochemical characteristics of Evans tumor occurring in the lung with a review of the literature and discuss the differential diagnosis in this exceptional localization. © The Author(s) 2024.

Citation

Aida Ayadi, Yoldez Houcine, Chirine Moussa, Houda Rouis, Tarek Abid, Begueret Hugues, François Le Loarer. Primary lung low-grade fibromyxoid sarcoma: A rare case with A diagnostic dilemma. Rare tumors. 2024;16:20363613241234201

PMID: 38435384

search → result